Medical Health Encyclopedia

Injury Disease Nutrition Poison Symptoms Surgery Test Special Topic
A B C D E F G H I J K L M N O P Q R S T U V W X Y Z
Clubbing Postural drainage Clubbed fingers Cystic fibrosis
Overview Symptoms Treatment Prevention
Cystic fibrosis
Treatment: An early diagnosis of CF and a comprehensive treatment plan can improve both survival and quality of life. Specialty clinics for cystic fibrosis may be helpful and can be found in many communities.   Treatment includes: Antibiotics for respiratory infections. Pancreatic enzymes to replace those that are missing. Vitamin supplements, especially vitamins A, D, E, and K. Inhaled bronchodilators, such as albuterol (Proventil, Ventolin), help open the airways. DNAse enzyme replacement therapy. The medication dornase (Pulmozyme) contains an enzyme that thins the mucus and makes it easier to cough up. Pain relievers. Research has shown that the pain reliever ibuprofen may slow lung deterioration in some children with cystic fibrosis. The results were most dramatic in children ages 5 to 13. Postural drainage and chest percussion. Lung transplant may be considered in some cases. Support Groups: Text Continues Below For additional information and resources, see cystic fibrosis support group. Expectations (prognosis): Disease registries now show that 40% of patients with cystic fibrosis are over age 18. Today, the average life span for those who live to adulthood is approximately 35 years, a dramatic increase over the last three decades. Death is usually caused by lung complications. Complications: The most common complications are chronic respiratory infections. Pneumonia, recurrent Pneumothorax Coughing up blood Chronic respiratory failure Cor pulmonale Liver disease Diabetes Osteoporosis and arthritis Page:  1 | 2 | Next >>